Inhibition of the mitochondrial respiratory chain complex activities in rat cerebral cortex by methylmalonic acid AM Brusque, RB Rosa, PF Schuck, KB Dalcin, CAJ Ribeiro, CG Silva, ... Neurochemistry international 40 (7), 593-601, 2002 | 136 | 2002 |
Inhibition of cytochrome c oxidase activity in rat cerebral cortex and human skeletal muscle by D-2-hydroxyglutaric acid in vitro CG Da Silva, CAJ Ribeiro, G Leipnitz, CS Dutra-Filho, ÂTS Wyse, ... Biochimica et Biophysica Acta (BBA)-Molecular Basis of Disease 1586 (1), 81-91, 2002 | 98 | 2002 |
Inhibition of brain energy metabolism by the α-keto acids accumulating in maple syrup urine disease AM Sgaravatti, RB Rosa, PF Schuck, CAJ Ribeiro, CMD Wannmacher, ... Biochimica et Biophysica Acta (BBA)-Molecular Basis of Disease 1639 (3), 232-238, 2003 | 96 | 2003 |
Evidence that quinolinic acid severely impairs energy metabolism through activation of NMDA receptors in striatum from developing rats CAJ Ribeiro, V Grando, CS Dutra Filho, CMD Wannmacher, M Wajner Journal of neurochemistry 99 (6), 1531-1542, 2006 | 76 | 2006 |
Inhibition of brain energy metabolism by the branched-chain amino acids accumulating in maple syrup urine disease CA Ribeiro, ÂM Sgaravatti, RB Rosa, PF Schuck, V Grando, AL Schmidt, ... Neurochemical research 33, 114-124, 2008 | 72 | 2008 |
Isovaleric Acid Reduces Na+, K+-ATPase Activity in Synaptic Membranes from Cerebral Cortex of Young Rats CAJ Ribeiro, F Balestro, V Grando, M Wajner Cellular and molecular neurobiology 27, 529-540, 2007 | 57 | 2007 |
Inhibition of creatine kinase activity from rat cerebral cortex by D-2-hydroxyglutaric acid in vitro CG Da Silva, ARF Bueno, PF Schuck, G Leipnitz, CAJ Ribeiro, RB Rosa, ... Neurochemistry international 44 (1), 45-52, 2004 | 56 | 2004 |
Inhibition of Creatine Kinase Activity in Vitro by Ethylmalonic Acid in Cerebral Cortex of Young Rats PF Schuck, G Leipnitz, CAJ Ribeiro, KB Dalcin, DR Assis, AG Barschak, ... Neurochemical research 27, 1633-1639, 2002 | 52 | 2002 |
Evidence that 3-hydroxyglutaric acid interacts with NMDA receptors in synaptic plasma membranes from cerebral cortex of young rats RB Rosa, C Schwarzbold, KB Dalcin, GC Ghisleni, CAJ Ribeiro, ... Neurochemistry international 45 (7), 1087-1094, 2004 | 48 | 2004 |
Inhibition of energy metabolism in cerebral cortex of young rats by the medium-chain fatty acids accumulating in MCAD deficiency DR de Assis, R de Cássia Maria, RB Rosa, PF Schuck, CAJ Ribeiro, ... Brain research 1030 (1), 141-151, 2004 | 43 | 2004 |
Ethylmalonic Acid Inhibits Mitochondrial Creatine Kinase Activity from Cerebral Cortex of Young Rats in Vitro G Leipnitz, PF Schuck, CAJ Ribeiro, KB Dalcin, DR Assis, AG Barschak, ... Neurochemical research 28, 771-777, 2003 | 42 | 2003 |
L-2-hydroxyglutaric acid inhibits mitochondrial creatine kinase activity from cerebellum of developing rats CG da Silva, ARF Bueno, PF Schuck, G Leipnitz, CAJ Ribeiro, ... International journal of developmental neuroscience 21 (4), 217-224, 2003 | 41 | 2003 |
Glutaric acid administration impairs energy metabolism in midbrain and skeletal muscle of young rats GC Ferreira, CM Viegas, PF Schuck, A Tonin, CAJ Ribeiro, DM Coelho, ... Neurochemical research 30, 1123-1131, 2005 | 35 | 2005 |
Evidence that glutaric acid reduces glutamate uptake by cerebral cortex of infant rats RB Rosa, KB Dalcin, AL Schmidt, D Gerhardt, CAJ Ribeiro, GC Ferreira, ... Life sciences 81 (25-26), 1668-1676, 2007 | 34 | 2007 |
Toxic synergism between quinolinic acid and organic acids accumulating in glutaric acidemia type I and in disorders of propionate metabolism in rat brain synaptosomes … AL Colín-González, AL Paz-Loyola, I Serratos, B Seminotti, CAJ Ribeiro, ... Neuroscience 308, 64-74, 2015 | 30 | 2015 |
Disruption of brain redox homeostasis in glutaryl-CoA dehydrogenase deficient mice treated with high dietary lysine supplementation B Seminotti, AU Amaral, MS da Rosa, CG Fernandes, G Leipnitz, ... Molecular genetics and metabolism 108 (1), 30-39, 2013 | 30 | 2013 |
Ethylmalonic acid impairs brain mitochondrial succinate and malate transport AU Amaral, C Cecatto, ENB Busanello, CAJ Ribeiro, DR Melo, G Leipnitz, ... Molecular genetics and metabolism 105 (1), 84-90, 2012 | 30 | 2012 |
Neurochemical evidence that 3-methylglutaric acid inhibits synaptic Na+, K+-ATPase activity probably through oxidative damage in brain cortex of young rats CAJ Ribeiro, FH Hickmann, M Wajner International Journal of Developmental Neuroscience 29 (1), 1-7, 2011 | 30 | 2011 |
Striatum is more vulnerable to oxidative damage induced by the metabolites accumulating in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency as compared to liver G Leipnitz, B Seminotti, CG Fernandes, AU Amaral, AP Beskow, ... International Journal of Developmental Neuroscience 27 (4), 351-356, 2009 | 30 | 2009 |
Bradykinin-potentiating PEPTIDE-10C, an argininosuccinate synthetase activator, protects against H2O2-induced oxidative stress in SH-SY5Y neuroblastoma cells SM Querobino, CAJ Ribeiro, C Alberto-Silva Peptides 103, 90-97, 2018 | 29 | 2018 |